Otosclerosis
TroyA.Hutchins,MD
KEYFACTS
NEXTTerminologyStartsperifenestral(FOto),progressestosurroundcochlea(FOto+COto)
Synonym:Otospongiosis
Types:Fenestralotosclerosis(FOto),cochlearotosclerosis(COto)
Pathologicappearanceoflyticspongybonefociinbonylabyrinthofunknowncause
Fissulaantefenestram:Cleftoffibrocartilaginoustissuebetweeninnermiddleearsjustanteriortoovalwindow
ImagingBestdiagnosticclue:TemporalboneCTshowslytic(otospongiotic)fociinvolvingbonylabyrinth
FOto:Startsatanteriormarginofovalwindow(fissulaantefenestram)
COto:Affectspericochlearbonylabyrinth
TopDifferentialDiagnosesChronicotitismediawithtympanosclerosis
TemporalbonePagetdisease
Temporalbonefibrousdysplasia
Temporalboneosteoradionecrosis
Temporalboneosteogenesisimperfecta
PathologyEnchondrallayerofbonylabyrinthdisplaysspongy,vascular,decalcified,irregularboneformation
ClinicalIssuesBilateralprogressiveconductive(FOto)ormixed(FOto+COto)hearinglossinyoungadult
DiagnosticChecklistTypicalotospongioticplaquesof"otosclerosis"arelyticaffectbonylabyrinth
TERMINOLOGY
PREVIOUSNEXTAbbreviationsFenestralotosclerosis(FOto)
Cochlearotosclerosis(COto)
SynonymsOtospongiosis,fenestralotospongiosis,cochlearotospongiosis
DefinitionsAlsocalled"cochlearcleft"
Startsperifenestral(FOto),progressestosurroundcochlea(FOto+COto)
Pathologicappearanceoflyticspongybonefociinbonylabyrinthofunknowncause
Fissulaantefenestram:Cleftoffibrocartilaginoustissuebetweeninnermiddleearsjustanteriortoovalwindow
IMAGING
PREVIOUSNEXTGeneralFeaturesFOto:Ovoidplaquesmost
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